IgA vasculitis

Target entity: IgA vasculitis
Context triple: [Chapel Hill Consensus Conference on Vasculitis Nomenclature, defines, IgA vasculitis]

• A. Wegener's granulomatosis
  Wegener's granulomatosis, now more commonly called granulomatosis with polyangiitis, is a rare autoimmune disease characterized by inflammation of blood vessels that can damage organs such as the lungs, kidneys, and upper respiratory tract.
• B. microscopic polyangiitis
  Microscopic polyangiitis is a rare autoimmune small-vessel vasculitis that causes inflammation and damage in organs such as the kidneys, lungs, and nerves, often associated with anti-neutrophil cytoplasmic antibodies (ANCA).
• C. Behçet's disease
  Behçet's disease is a rare, chronic inflammatory disorder characterized by recurrent mouth and genital ulcers, eye inflammation, and systemic vasculitis affecting multiple organ systems.
• D. erythema nodosum
  Erythema nodosum is an inflammatory condition characterized by tender red nodules, usually on the shins, often associated with systemic diseases such as infections, autoimmune disorders, and inflammatory bowel disease.
• E. Mikulicz disease
  Mikulicz disease is a rare chronic condition characterized by painless, symmetrical enlargement of the lacrimal and salivary glands, historically considered a form of benign lymphoepithelial lesion and now often associated with IgG4-related disease.
• F. None of above. chosen
• G. Unsure - the case is ambiguous/there is not enough information to decide.

Target entity: IgA vasculitis
Target entity description: IgA vasculitis is an immune complex–mediated small-vessel vasculitis, typically characterized by IgA deposition in vessel walls and presenting with palpable purpura, arthralgia, abdominal pain, and renal involvement, especially in children.

• A. Wegener's granulomatosis
  Wegener's granulomatosis, now more commonly called granulomatosis with polyangiitis, is a rare autoimmune disease characterized by inflammation of blood vessels that can damage organs such as the lungs, kidneys, and upper respiratory tract.
• B. microscopic polyangiitis
  Microscopic polyangiitis is a rare autoimmune small-vessel vasculitis that causes inflammation and damage in organs such as the kidneys, lungs, and nerves, often associated with anti-neutrophil cytoplasmic antibodies (ANCA).
• C. Behçet's disease
  Behçet's disease is a rare, chronic inflammatory disorder characterized by recurrent mouth and genital ulcers, eye inflammation, and systemic vasculitis affecting multiple organ systems.
• D. erythema nodosum
  Erythema nodosum is an inflammatory condition characterized by tender red nodules, usually on the shins, often associated with systemic diseases such as infections, autoimmune disorders, and inflammatory bowel disease.
• E. Mikulicz disease
  Mikulicz disease is a rare chronic condition characterized by painless, symmetrical enlargement of the lacrimal and salivary glands, historically considered a form of benign lymphoepithelial lesion and now often associated with IgG4-related disease.
• F. None of above. chosen